日日操日日操,亚洲日本午夜激情,人妻内射精品一区二区,国产一区北条麻妃

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
亚洲做性AV,2亚洲精品一区二区
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-Argininosuccinate Lyase/Gold Conjugated antibody (bs-12515R-Gold)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-12515R-Gold
英文名稱 Rabbit Anti-Argininosuccinate Lyase/Gold Conjugated antibody
中文名稱 膠體金標記的琥珀酸裂解酶抗體
別    名 Argininosuccinase; Argininosuccinate lyase; Arginosuccinase; ARLY_HUMAN; ASAL; ASL; EC 4.3.2.1.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul(10nm  15nm  35nm
研究領(lǐng)域 腫瘤  細胞生物  信號轉(zhuǎn)導(dǎo)  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Horse, )
產(chǎn)品應(yīng)用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 52kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ASL/Argininosuccinate Lyase
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產(chǎn)品介紹 background:
This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008]

Function:
Amino-acid biosynthesis; L-arginine biosynthesis; L-arginine from L-ornithine and carbamoyl phosphate: step 3/3.
Nitrogen metabolism; urea cycle; L-arginine and fumarate from (N(omega)-L-arginino)succinate: step 1/1.

Subcellular Location:
Acetylation modifies enzyme activity in response to alterations of extracellular nutrient availability. Acetylation increased with trichostin A (TSA) or with nicotinamide (NAM). Glucose increases acetylation by about a factor of 3 with decreasing enzyme activity. Acetylation on Lys-288 is decreased on the addition of extra amino acids resulting in activation of enzyme activity.

DISEASE:
Defects in ASL are the cause of arginosuccinicaciduria (ARGINSA) [MIM:207900]. Arginosuccinicaciduria is an autosomal recessive disorder of the urea cycle. The disease is characterized by mental and physical retardation, liver enlargement, skin lesions, dry and brittle hair showing trichorrhexis nodosa microscopically and fluorescing red, convulsions, and episodic unconsciousness.

Similarity:
Belongs to the lyase 1 family. Argininosuccinate lyase subfamily.

Database links:

Entrez Gene: 435 Human

Entrez Gene: 109900 Mouse

Entrez Gene: 59085 Rat

Entrez Gene: 512771 Cow

Omim: 608310 Human

SwissProt: Q3SZJ0 Cow

SwissProt: P04424 Human

SwissProt: Q91YI0 Mouse

SwissProt: P20673 Rat

Unigene: 632015 Human

Unigene: 23869 Mouse

Unigene: 64591 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 m.bklrv.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
久国产精品欧美一区| 日韩24小时精品视频在线一区二区| 美女毛片视频久| 亚洲乱码精品久久久久| 操美女骚逼视频聊天| 日本电影人妻久久久| 欧美色亚洲色网站| 日本欧美做爱| 美女激情吸奶舔下面一区二区二| 日韩第一精品在线| 人人爽人人爽人人爽av片特级| 欧美激情日韩精品五月婷婷在线观看| 成人av黄色小说| 欧美国产精品九一| 最黄色AV| 亚洲AV夜夜| 亚洲熟女重口味视频| 麻豆99国产99精品999| 在线电影中文字幕麻豆| 人人人午夜网| 人妻视频网站| 日本在线观看一区二区| 欧美日韩成人在线不卡视频| 国综合一区二区| 国产欧美一区二区精品每日更新 | 欧美中文阿V精品一线| 尤物久久99国产综| 国内毛片一区二区三区| 国产搞逼视频网址| 超碰一区二区 在线| 中文字幕在线观看婷婷基地| 尤物在线不卡国产| 国产精品婷婷色一区二区| 欧美日韩高清国产精品| 美女人妻在线导航| 色欲精品一区| 二区在线播放9| www蜜臀| 好看的大鸡巴操逼片| 国产一级成人电影| 超碰成人最新|