日日操日日操,亚洲日本午夜激情,人妻内射精品一区二区,国产一区北条麻妃

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
日韩女同一区二区,哥要色中文一区二区三区
Rabbit Anti-Argininosuccinate Lyase/Cy5 Conjugated antibody (bs-12515R-Cy5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-12515R-Cy5
英文名稱 Rabbit Anti-Argininosuccinate Lyase/Cy5 Conjugated antibody
中文名稱 Cy5標(biāo)記的琥珀酸裂解酶抗體
別    名 Argininosuccinase; Argininosuccinate lyase; Arginosuccinase; ARLY_HUMAN; ASAL; ASL; EC 4.3.2.1.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細胞生物  信號轉(zhuǎn)導(dǎo)  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Horse, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 52kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ASL/Argininosuccinate Lyase
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008]

Function:
Amino-acid biosynthesis; L-arginine biosynthesis; L-arginine from L-ornithine and carbamoyl phosphate: step 3/3.
Nitrogen metabolism; urea cycle; L-arginine and fumarate from (N(omega)-L-arginino)succinate: step 1/1.

Subcellular Location:
Acetylation modifies enzyme activity in response to alterations of extracellular nutrient availability. Acetylation increased with trichostin A (TSA) or with nicotinamide (NAM). Glucose increases acetylation by about a factor of 3 with decreasing enzyme activity. Acetylation on Lys-288 is decreased on the addition of extra amino acids resulting in activation of enzyme activity.

DISEASE:
Defects in ASL are the cause of arginosuccinicaciduria (ARGINSA) [MIM:207900]. Arginosuccinicaciduria is an autosomal recessive disorder of the urea cycle. The disease is characterized by mental and physical retardation, liver enlargement, skin lesions, dry and brittle hair showing trichorrhexis nodosa microscopically and fluorescing red, convulsions, and episodic unconsciousness.

Similarity:
Belongs to the lyase 1 family. Argininosuccinate lyase subfamily.

Database links:

Entrez Gene: 435 Human

Entrez Gene: 109900 Mouse

Entrez Gene: 59085 Rat

Entrez Gene: 512771 Cow

Omim: 608310 Human

SwissProt: Q3SZJ0 Cow

SwissProt: P04424 Human

SwissProt: Q91YI0 Mouse

SwissProt: P20673 Rat

Unigene: 632015 Human

Unigene: 23869 Mouse

Unigene: 64591 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 m.bklrv.cn 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
美女一区国产91| 日本道男人天下一区二区三区| 国产剧情亚洲一区二区| 美女主播三级在线| 男女xxx| 午夜福利视频韩国伦理电影| 欧美日本韩国国产插无码| 天天综合网久久综合网黄色小说| 中文无码精品久久久字幕| 人妻视频在线观看区| 婷婷亚洲卡一| 国产精品一区二区三区毛片| 久久精品视频丰满| 久久AV日日骚| 亚洲中文字幕欧美一区| 美日韩精品久久久| 色狠狠久久αⅴ北条麻妃| 免费精品久久久韩国| 国产经典日韩欧美一区二区| 国产福利精品视频福利| 亚洲精品少妇久久| 国产色播| 手机青青在线播放香蕉| 国产激情精彩| 日本邪恶影院A| 午夜生活在线看 粗| 日韩国产第一页免费| 久久黄香蕉黄色| 精品人妻中文字幕视频| 黄色91av一区| 黄色大片国产精品久久| 亚洲AV成人一区二区三区久久| 日韩一级爽视频| 日本精品播放| 97se综合一区二区三区| 成人丁香永久免费视频| 国产精华网在线观看视频| 久久久久精品九一蜜桃 | 欧美黄色片免| 久久精品鸡巴视频| 欧美精品一区二区久久婷婷|