日日操日日操,亚洲日本午夜激情,人妻内射精品一区二区,国产一区北条麻妃

掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質(zhì)量反饋  關于我們  聯(lián)系我們
成人综合视频在线观看的,日本二区九九,jk足交一区二区
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-Fumarylacetoacetate hydrolase/RBITC Conjugated antibody (bs-16194R-RBITC)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-16194R-RBITC
英文名稱 Rabbit Anti-Fumarylacetoacetate hydrolase/RBITC Conjugated antibody
中文名稱 羅丹明(RBITC)標記的延胡索酰乙酰乙酸水解酶抗體
別    名 Beta diketonase; FAA; FAAA_HUMAN; FAH; Fumarylacetoacetase; Fumarylacetoacetate; Fumarylacetoacetate hydrolase.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 腫瘤  細胞生物  免疫學  細胞骨架  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Pig, )
產(chǎn)品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 47kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Fumarylacetoacetate hydrolase
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008]

Function:
Fumarylacetoacetate hydrolase is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). This is an autosomal recessive inborn error of metabolism that occurs in both an acute and a chronic form. Clinical characteristics of the acute form include hepatic failure and death in infancy, whereas children with the chronic form have renal tubular dysfunction and hypophosphatemic rickets, progressive liver disease with development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment.

Subunit:
Homodimer.

Tissue Specificity:
Mainly expressed in liver and kidney. Lower levels are also detected in many other tissues.

Similarity:
Belongs to the FAH family.

Database links:

Entrez Gene: 2184 Human

Entrez Gene: 14085 Mouse

Entrez Gene: 29383 Rat

Omim: 613871 Human

SwissProt: P16930 Human

SwissProt: P35505 Mouse

SwissProt: P25093 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 m.bklrv.cn 北京博奧森生物技術有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
欧美人妻精品99w| 欧美天天一区| 久久精品国产麻豆产毛片能回酒店| 国产 欧美一区二区三区大长颈| 日韩欧美亚洲综合图| 久热人妻二区| 亚洲精品黄暴AV!| 3.com中文字幕| 按摩亚洲一区| xxx噢美潮喷直播| 亚洲美女一区二区三区| 999一区二区三在线| 双飞丰满少妇熟女视频| 日韩欧美在线有限| 中文音像视频一区二区| 中文字幕日韩无码电影| 拜泉县| 国产精品 I8禁| 处文一级黄色按摩片播放| 色米米一区二区三区| 日韩精品cao在线| 无码免费AAAAAAAAA软件| 伊人aVPN综合网| 99热这里只有精品国产18| 日韩精品第一页在| 人人肏 欧美| 色综合四| 三级黄色香蕉视频| 婷婷五月天激情综合AV| 人人妻人人澡人人舔| 精品一线二线三线久久久久久久| 亚洲熟少黑人无码二区| 国产男女操逼内射高中| 中文久久久久久久久久久久h| 国产 中出 内射| 欧美老熟妇50 60 70m| 日韩在线成人手机视频| 久久午夜影院电影| 亚洲综合诱惑一区| 日韩欧美私色坊综合网88| 欧美一级精品在线|