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Rabbit Anti-HOGA1/Gold Conjugated antibody (bs-17348R-Gold)
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說 明 書: 100ul(10nm  15nm  35nm
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-17348R-Gold
英文名稱 Rabbit Anti-HOGA1/Gold Conjugated antibody
中文名稱 膠體金標(biāo)記的HOGA1蛋白抗體
別    名 4 hydroxy 2 oxoglutarate aldolase 1; C10orf65; DHDPS like protein; DHDPS2; DHDPSL; Dihydrodipicolinate synthase like; Dihydrodipicolinate synthase like, mitochondrial; Dihydrodipicolinate synthetase homolog 2; FLJ37472; HOGA1; HOGA1_HUMAN; HP3; mitochondrial; N acetylneuraminate pyruvate lyase 2 (putative); NPL2; Probable 2 keto 4 hydroxyglutarate aldolase; Probable 4 hydroxy 2 oxoglutarate aldolase mitochondrial; Probable 4-hydroxy-2-oxoglutarate aldolase; Probable KHG aldolase; Protein 569272.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說 明 書 100ul(10nm  15nm  35nm
研究領(lǐng)域 細(xì)胞生物  信號(hào)轉(zhuǎn)導(dǎo)  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Mouse,  (predicted: Human, )
產(chǎn)品應(yīng)用 IEM=1:20-200 ICA=1:20-200 ChIP=1:20-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 32kDa
性    狀 Lyophilized or Liquid
濃    度 0.4mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human HOGA1
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.02M TBS(pH8.2) with 1% BSA, 0.03% Proclin300.
保存條件 Store at 2-8 oC for 3-6 months. Avoid repeated freeze/thaw cycles.
產(chǎn)品介紹 background:
DHDPSL is a 327 amino acid mitochondrial protein that catalyzes the last step in the hydroxyproline metabolic pathway. Existing as two alternatively spliced isoforms, DHDPSL is expressed in kidney and liver and is inhibited by divalent cations. Defects in the gene that encode DHDPSL are the cause of primary hyperoxalurea type III (HP3), a disorder of calcium oxalate nephrolithiasis. Patients with HP3 excrete urine with elevated levels of oxalate and L-glycerate. The DHDPSL gene maps to human chromosome 10, which contains over 800 genes and 135 million nucleotides. Defects in some of the genes that map to chromosome 10 are associated with Charcot-Marie Tooth disease, Jackson-Weiss syndrome, Usher syndrome, nonsyndromatic deafness, Wolman’s syndrome, Cowden syndrome, multiple endocrine neoplasia type 2 and porphyria

Database links:

Entrez Gene: 112817 Human

Entrez Gene: 67432 Mouse

Entrez Gene: 293949 Rat

Omim: 613597 Human

SwissProt: Q86XE5 Human

SwissProt: Q9DCU9 Mouse

Unigene: 180346 Human

Unigene: 24196 Mouse

Unigene: 13905 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
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